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KMID : 0383820070630030289
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Tuberculosis and Respiratory Diseases
2007 Volume.63 No. 3 p.289 ~ p.293
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A Case of Lymphangioleiomyomatosis Presenting as a Lung Mass
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Park Seon-Cheol
Park Moo-Suk
Kim Se-Kyu
Chang Joon
Kim Sung-Kyu
Kim Young-Sam
Kwon Ji-Eun
Jeon Han-Ho
Park Byung-Hoon
Shin Sang-Yun
Jung Kyung-Soo
Jeong Jae-Heon
Park Jun-Chul
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Abstract
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Lymphangioleiomyomatosis (LAM) is a rare disease that affects females of reproductive age. It is characterized by the abnormal proliferation of smooth muscle cells in the lung and along the axial lymphatics. We report a case of lymphangioleiomyomatosis presenting as a lung mass. The patient visited the emergency room because of dyspnea upon exertion. The chest X-ray showed a lung mass in the right lower lung field and a pneumothorax in the left lung. Chest computed tomography revealed a 5 x 3 cm sized mass in the right lower lobe and multiple thin-walled small cysts scattered in both lungs. Transbronchial biopsy of the lung mass was performed. The biopsy specimen showed atypical smooth muscle cell proliferation and cystic dilatation of the terminal bronchioles, which confirmed the diagnosis of lymphangioleiomyomatosis. To the best of our knowledge, this is the first case of lymphangioleiomyomatosis presenting as a lung mass.
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KEYWORD
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Lymphangioleiomyomatosis, Lung mass
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